Elephantiasis neuromatosa of the lower limb in a patient with neurofibromatosis type-1: A case report with imaging findings
نویسندگان
چکیده
منابع مشابه
Giant elephantiasis neuromatosa in the setting of neurofibromatosis type 1: A case report.
Elephantiasis neuromatosa (EN) can arise from a plexiform neurofibroma of the superficial and deep nerves developing from a hyperproliferation of the perineural connective tissue infiltrating adjacent fat and muscles. To date, the clinical association between EN and neurofibromatosis type 1 (NF1) has been poorly defined, particularly with regard to the role of lymphatic alterations and the cons...
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ژورنال
عنوان ژورنال: Journal of Pediatric Neurosciences
سال: 2010
ISSN: 1817-1745
DOI: 10.4103/1817-1745.66684